Regina Gironés
Pulmonary lymphangiomyomatosis (LAMP) is a rare, progressive and fatal interstitial lung disease that affects women of childbearing age. Its association with neoplasms, mostly renal angiomyolipomas, has previously been reported. Association with lung cancer has also been documented; however there are very few reported cases. We reported a case of a 42-year-old woman who presented with hemoptysis. Chest x-ray and computed tomography findings suggested LAMP. A lung biopsy was done, and pathological examination diagnosed LAMP and synchronous lung adenocarcinoma. Positron emission tomography with (18)F-fluorodesoxyglucose (PET-TAC FDG) after surgery did not identify pathologic uptake. At follow up, another suspicious lung nodule was found. Removal showed another lung adenocarcinoma. No more nodules have been found. This is the first case of synchronous adenocarcinoma resected twice in combination with LAMP.